产品名称 | MTCO2 Rabbit mab |
产品货号 | AFRM9036 |
基因名称 | MT-CO2 COII COXII MTCO2 |
蛋白名称 | Cytochrome c oxidase subunit 2 (Cytochrome c oxidase polypeptide II) |
Gene ID | Human:4513     |
SwissPro | Human:P00403     |
宿主种属 | Rabbit |
应用范围 | WB;IHC;IF;IP;ELISA |
稀释比例 | IHC 1:200-1000,WB 1:1000-5000,IF 1:200-1000,ELISA 1:5000-20000,IP 1:50-200 |
反应种属 | Human; |
克隆性 | Monoclonal |
克隆号 | AFKL9036 |
特异性 | endogenous |
同种型 | Rabbit IgG |
保存液 | PBS, 50% glycerol, 0.05% Proclin 300, 0.05%BSA |
纯化方式 | Protein A |
保存条件 | -20°C/1 year |
背景资料 | 21kD |
产品概述 | cofactor:Copper A.,disease:Defects in MT-CO2 are a cause of cytochrome c oxidase deficiency (COX deficiency) [MIM:220110]; also called mitochondrial complex IV deficiency. COX deficiency is a clinically heterogeneous disorder. The clinical features are ranging from isolated myopathy to severe multisystem disease, with onset from infancy to adulthood.,disease:Defects in MT-CO2 are associated with tumor formation.,function:Cytochrome c oxidase is the component of the respiratory chain that catalyz |